Two Cases of Tuberous Sclerosis With Multiple Rhabdomyoma Succumbing to Sudden Cardiac Death

Tuberous sclerosis complex is an autosomal dominant condition with variable penetrance. It characterized by tuberose deposits in various organ systems. Although clinical features predominate neurocutaneous manifestations, cardiac, kidney, and lung involvement are common. Cardiac marked the presence of multiple rhabdomyomas some cases arrhythmias. In absence symptoms, require no specific treatment. However, cardiac arrhythmias unpredictable may be cause sudden death cases. treatment mainly symptomatic, drugs like rapamycin have shown promise regression astrocytomas angiofibromas. Here, we reporting two tuberous which one succumbed to other possible death.